PubMed journal article [Idiopathic pulmonary hemosiderosis were found in PRIME PubMed. Download Source. Revista chilena de pediatrĂ­a pg PubMed journal article [Idiopathic pulmonary hemosiderosis: review of literature and case report were found in La Pediatria Sep 30 pg Revista Cubana de PediatrĂ­a Idiopathic pulmonary hemosiderosis is those processes characterized by anomalous depots of hemosiderin in the pulmonary.

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J Clin Case Rep. Pulmonary hemosiderosis PH is a rare disease that may occur at any age, although it generally affects children, with an estimated incidence of 0. Please review our privacy policy. The clinical suspicion of alveolar hemorrhage was raised by the lack of response to iron therapy, with a progressive decrease in Hb levels and after extensive investigation of other potential sources of bleeding.

The magazine, referring to the Spanish-speaking pediatric, indexed in major international databases: Vitamin B 12 and folic acid were within normal range and the bone marrow smear was compatible with sideropenia. Idiopathic PH has been associated with celiac disease and, therefore, this condition should be excluded in these patients. You can change the settings or obtain more information by clicking here. To improve our services and products, we use “cookies” own or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior.


Idiopathic pulmonary hemosiderosis – a diagnostic challenge.


Are you a health professional able to prescribe or dispense drugs? Gastrointestinal bleeding was ruled out pediaatria negative extensive etiological investigation. He was initiated on corticosteroid therapy, later associated to an immunosuppressive agent, with subsequent correction of anemia and of the radiological pattern.

Long-term prednisone and azathioprine treatment of hemosideross patient with idiopathic pulmonary hemosiderosis. Contudo, o acompanhamento da paciente por quatro anos afastou estas possibilidades, bem como a possibilidade de colagenoses e vasculites. For this reason, he was not submitted to an upper esophagogastroduodenoscospy, as previously planned.

A favorable prognosis may be expected in our case, as there were no major episodes of hemorrhage and response to therapy was favorable. Diffuse alveolar hemorrhage is caused by loss of integrity of the basement membrane of pulmonary capillaries, with consequent leakage of blood into the alveolar space. This case highlights the importance of including chest radiography in the investigation of blood loss of unknown origin. On the other hand, the rarity of the alveolar hemorrhage and the variability of the clinical course frequently result in a delay in the diagnosis.

Idiopathic pulmonary hemosiderosis treated with azathioprine in a child

After excluding the most frequent causes of PH: Open in a separate window. Author information Article notes Copyright and License information Disclaimer. There are several known causes of diffuse alveolar hemorrhage vasculitides, connective tissue disorders, Heiner’s syndrome, cardiovascular diseases, among others.


J Paediatr Child Health. Bronchoalveolar lavage fluid showing numerous pediatrua macrophages stained positive with Perls.

Acute respiratory insufficiency as debut of idiopathic pulmonary hemosiderosis in an infant. We present the case of a 4 year-old child presenting with hemosiderosia, vomiting and prostration, associated with pallor. Pulmonary hemorrhage can also be confirmed by the identification of hemosiderin-laden macrophages in the bronchoalveolar lavage fluid. Subscribe to our Newsletter.

He was pale, prostrated and tachypneic, with dispersed bilateral rhonchi on pulmonary auscultation. Subsequently, there was laboratory improvement and corticosteroid was tapered. As such, given the iron-deficiency anemia with characteristics compatible with blood loss although not identifiedand despite the absence of respiratory symptoms at this phase, we started looking for other sources of hemorrhage, namely epdiatria.

Si continua navegando, consideramos que acepta su peditaria. A physician survey reveals differences in management of idiopathic pulmonary hemosiderosis. Analytically he had Hb of 2.

SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact. Idiopathic pulmonary hemosiderosis in adults: After the etiological study, the diagnosis of idiopathic pulmonary hemosiderosis was made by exclusion.